Acroangiodermatitis
Synopsis

Stewart-Bluefarb syndrome refers to acroangiodermatitis arising in the setting of congenital arteriovenous malformations, typically on the lower extremities. The condition is often diagnosed in teenagers or young adults.
The pathophysiology of acroangiodermatitis remains unclear. Some studies suggest that increased production of vasogenic growth factors, following disruption of normal cutaneous vascular perfusion, may play a role.
Codes
I78.9 – Disease of capillaries, unspecified
SNOMEDCT:
769036006 – Acroangiodermatitis of skin
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Last Updated:11/22/2020